Clinical, radiographic and lung function features of diffuse congenital cystic adenomatoid malformation of the lung in an adult.
نویسندگان
چکیده
Congenital cystic adenomatoid malformation of the bronchi with bilateral lung involvement has only previously been reported in one possible adult case. This report describes a young man with bilateral diffuse lung involvement, characteristic histological features, and a mixed restrictive/obstructive lung function pattern.
منابع مشابه
Congenital Cystic Adenomatoid Malformation (CCAM) of Lung in an Infant: A Case Report from Jammu & Kashmir, Northern India
Congenital cystic Adenomatoid malformation is a rare developmental abnormality of the lung occuring in 1-4/100000 live births.In most cases the outcome with CCAM in fetus is very good,while in some cases the outcome is very bad and can be life threatning for the fetus.we report here a case of 40 day old female infant who presented with worsening respiratory distress since birth and x ray and CT...
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ورودعنوان ژورنال:
- Minerva chirurgica
دوره 52 4 شماره
صفحات -
تاریخ انتشار 1997